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020 _a9783319460284
_9978-3-319-46028-4
024 7 _a10.1007/978-3-319-46028-4
_2doi
035 _a(DE-He213)978-3-319-46028-4
050 4 _aRC681-688.2
072 7 _aMJD
_2bicssc
072 7 _aMED010000
_2bisacsh
082 0 4 _a616.12
_223
245 1 0 _aPulmonary Hypertension in Adult Congenital Heart Disease
_h[electronic resource] /
_cedited by Konstantinos Dimopoulos, Gerhard-Paul Diller.
264 1 _aCham :
_bSpringer International Publishing :
_bImprint: Springer,
_c2017.
300 _aXV, 368 p. 82 illus., 46 illus. in color.
_bonline resource.
336 _atext
_btxt
_2rdacontent
337 _acomputer
_bc
_2rdamedia
338 _aonline resource
_bcr
_2rdacarrier
347 _atext file
_bPDF
_2rda
490 1 _aCongenital Heart Disease in Adolescents and Adults,
_x2364-6659
505 0 _aPart 1: Pathophysiology and Classification of Pulmonary Hypertension in Adult Congenital Heart Disease --  1. Congenital Heart Defects and Pulmonary Hypertension: The Heath Edwards Paradigm -- 2. Definition and Classification of Pulmonary Hypertension in Congenital Heart Disease -- 3. Eisenmenger Syndrome: Pathophysiology and Hematologic Effects -- 4. PAH in Patients with Persistent Systemic-Pulmonary Shunts and PAH in Patients with Small Cardiac Defects -- 5. Pulmonary Arterial Hypertension in Patients with Previous Reparative Surgery -- 6. Segmental Pulmonary Hypertension -- 7. Pulmonary Vascular Disease in Patients with Fontan-Type Circulation -- 8. Post-Capillary Pulmonary Hypertension in ACHD -- Part 2: The Diagnosis of Pulmonary Hypertension in Adult Congenital Heart Disease --  9. Physical Examination and Electrocardiography in Patients with Pulmonary Arterial Hypertension due to Congenital Heart Disease: Initial Clinical Assessment -- 10. The Role of Plain Chest Radiography and Computed Tomography -- 11. Echocardiography in the Diagnosis and Follow-up of Patients with Pulmonary Arterial Hypertension Associated with Congenital Heart Disease -- 12. Cardiovascular Magnetic Resonance -- 13. Cardiopulmonary Exercise and Six-minute Walk Testing -- 14. Cardiac Catheterization -- Part 3: Management of Pulmonary Hypertension in Adult Congenital Heart Disease -- 15. Conservative Management and Recommendations for PAH-CHD -- 16. Pulmonary Vasodilators in Patients with Pulmonary Arterial Hypertension Related to Congenital Heart Disease -- 17. Perspectives on Shunts in Pulmonary Arterial Hypertension: from Interventions to Create Shunts to the Concept of “Treat-and-Repair” -- 18. Eisenmenger Syndrome in Patients with Down’s Syndrome -- 19. Pregnancy and Contraception -- 20. Training and Recommendations for Exercise --  21. Prognostication in PAH-CHD -- 22. Management of Fontan patients -- 23. Palliative Care and End of Life Considerations in Patients with PAH-CHD -- 24. PAH in ACHD: Research, Global Perspective and Future Prospects: An Epilogue.  .
520 _aThis book is intended as a comprehensive, practically oriented reference on pulmonary hypertension within the context of adult congenital heart disease (ACHD). After an introductory chapter on pathophysiology, the various types of pulmonary hypertension that may be encountered in ACHD are discussed, highlighting the specifics observed within different patient categories. The diagnostic approach is then addressed in detail, and the last section of the book is devoted to management options, from conservative approaches to interventional treatment and the concept of treat and repair. Management in specific patient subjects, such as pregnant women, Fontan patients, and Down syndrome patients with Eisenmenger syndrome, is fully discussed, and guidance is also provided on palliative care.  Pulmonary arterial hypertension related to congenital heart disease (PAH-CHD), despite significant similarities in lung pathohysiology, differs significantly from other types of PAH in terms of mechanism of onset, natural history and management. Mistakes and pitfalls in the management of patients with PAH-CHD are often related to a lack of knowledge or expertise in this condition. Pulmonary Hypertension in Adult Congenital Heart Disease will be a valuable resource and learning tool for all who care for patients with ACHD, both in tertiary practice and general cardiology.
650 0 _aMedicine.
650 0 _aCardiology.
650 0 _aRespiratory organs
_xDiseases.
650 0 _aCardiac surgery.
650 1 4 _aMedicine & Public Health.
650 2 4 _aCardiology.
650 2 4 _aCardiac surgery.
650 2 4 _aPneumology/Respiratory System.
700 1 _aDimopoulos, Konstantinos.
_eeditor.
700 1 _aDiller, Gerhard-Paul.
_eeditor.
710 2 _aSpringerLink (Online service)
773 0 _tSpringer eBooks
776 0 8 _iPrinted edition:
_z9783319460260
830 0 _aCongenital Heart Disease in Adolescents and Adults,
_x2364-6659
856 4 0 _uhttp://dx.doi.org/10.1007/978-3-319-46028-4
912 _aZDB-2-SME
999 _c6766
_d6766