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001 60047
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008 170109s2017 gw | s |||| 0|eng d
020 _a9783319413495
_9978-3-319-41349-5
024 7 _a10.1007/978-3-319-41349-5
_2doi
035 _a(DE-He213)978-3-319-41349-5
050 4 _aRC927-927.5
072 7 _aMJM
_2bicssc
072 7 _aMED083000
_2bisacsh
082 0 4 _a616.723
_223
245 1 0 _aSystemic Fibroinflammatory Disorders
_h[electronic resource] /
_cedited by Augusto Vaglio.
264 1 _aCham :
_bSpringer International Publishing :
_bImprint: Springer,
_c2017.
300 _aXII, 243 p. 33 illus., 22 illus. in color.
_bonline resource.
336 _atext
_btxt
_2rdacontent
337 _acomputer
_bc
_2rdamedia
338 _aonline resource
_bcr
_2rdacarrier
347 _atext file
_bPDF
_2rda
490 1 _aRare Diseases of the Immune System,
_x2282-6505
505 0 _aPreface -- 1 Genetics of fibro-inflammatory disorders -- 2 Basic mechanisms linking inflammation and fibrosis -- 3 Histopathology of systemic fibro-inflammatory disorders -- 4 IgG4-related disorders: clinical and therapeutic aspects -- 5 IgG4-related disorders: pathophysiology -- 6 IgG4-related nephropathy -- 7 Autoimmune (IgG4-related) pancreatitis and sclerosing cholangitis -- 8 Sclerosing forms of autoimmune thyroiditis: from Hashimoto’s to Riedel’s to IgG4-related forms -- 9 Chronic periaortitis/retroperitoneal fibrosis: overview -- 10 Diffuse periaortitis -- 11 Treatment of chronic periaortitis/retroperitoneal fibrosis -- 12 Mediastinal fibrosis -- 13 Erdheim-Chester disease -- 14 Nephrogenic systemic fibrosis -- 15 Sclerosing mesenteritis -- 16 Malignant diseases mimicking retroperitoneal fibrosing disorders -- Subject Index.
520 _aThis book provides detailed information on the nosology, pathology, pathogenesis, clinical presentation, diagnosis and treatment of fibro-inflammatory disorders, rare diseases that often display systemic organ involvement. Among the conditions considered are IgG4-related disease, sclerosing cholangitis, Hashimoto’s and Riedel’s thyroiditis, retroperitoneal fibrosis/chronic periaortitis, mediastinal fibrosis, Erdheim-Chester disease, gadolinium-induced fibrosis, and sclerosing mesenteritis. This group of entities is still poorly defined and is characterized by the common denominator of chronic inflammatory infiltrate admixed with abundant fibrosis. IgG4-related disease is the prototypical example. Systemic Fibroinflammatory Disorders is the first book to draw together information on these conditions. As these diseases often require an interdisciplinary approach, the book is addressed to specialists of different disciplines, especially internists, rheumatologists, nephrologists, clinical immunologists, and hematologists.
650 0 _aMedicine.
650 0 _aImmunology.
650 0 _aNephrology.
650 0 _aRheumatology.
650 1 4 _aMedicine & Public Health.
650 2 4 _aRheumatology.
650 2 4 _aImmunology.
650 2 4 _aNephrology.
700 1 _aVaglio, Augusto.
_eeditor.
710 2 _aSpringerLink (Online service)
773 0 _tSpringer eBooks
776 0 8 _iPrinted edition:
_z9783319413471
830 0 _aRare Diseases of the Immune System,
_x2282-6505
856 4 0 _uhttp://dx.doi.org/10.1007/978-3-319-41349-5
912 _aZDB-2-SME
999 _c7941
_d7941